Laquievre Antoine; Hitier Martin; Petit Thierry; Ravasse Philippe & Rod Julien

We report the first case of a newborn presenting with a celio-mesenteric trunk variation associated with a giant omphalocele. The celio-mesenteric trunk was unexpected and unseen during the staged surgical closure. After partial reintegration of the liver, the newborn presented refractory hypovolemia with anuria, leading to redo surgery. This procedure revealed ischemia of the liver and necrosis of the entire gastrointestinal tract except the colon. Despite treatment, including liver externalization, the infant did not survive.The autopsy revealed a celio-mesenteric trunk, a rare anomaly characterized by a common origin of the celiac axis and the superior mesenteric artery from the aorta. This association may explain the dramatic consequences of the staged closure procedure. Awareness of the association of celio-mesenteric trunk and omphalocele would allow the surgeon to take extra care during this delicate surgery.

KEY WORDS: Celio-mesenteric trunk; Mesenteric arterial variation; Mesenteric ischemia; Giant omphalocele; Sodium valproate.

LAQUIEVRE, A.; HITIER, M.; PETIT, T.; RAVASSE, P. & ROD, J. Celio-mesenteric trunk associated with giant omphalocele: surgical consequences. Int. J. Morphol., 35(3):938-941, 2017.